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KMID : 0364020180510030223
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Korean Journal of Thoracic and Cardiovascular Surgery
2018 Volume.51 No. 3 p.223 ~ p.226
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Erdheim-Chester Disease Presenting as an Anterior Mediastinal Tumor without Skeletal Involvement
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Lee Kang-Hoon
Kim Hyeong-Ryul
Roh Jin
Ok You-Jung
Jeon Bo-Bae
Kim Young-Woong
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Abstract
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Erdheim-Chester disease (ECD) is a form of non?Langerhans cell histiocytosis that most commonly involves the skeletal system. We report an unusual case of ECD presenting as an anterior mediastinal tumor without skeletal involvement. A 60-year-old man with no remarkable medical history was referred for evaluation of a mediastinal mass. The patient underwent surgical excision of the tumor via video-assisted thoracoscopic surgery. Histologic examination revealed marked proliferation of atypical histiocytes with sclerosis, and the results of immunohistochemical staining were suggestive of ECD.
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KEYWORD
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Erdheim-Chester disease, Histiocytosis, Non-Langerhans cell, Mediastinum, Video-assisted thoracic surgery
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